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HHT Mutation Database
Hereditary Hemorrhagic Telangiectasia
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Variants
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Gene Name
Location
DNA Change
Protein Change
Avg. Het. Frequency
Reference
Admin
ACVRL1
ENG
-
-
Showing 1 to 31 of 31.
ACVRL1
3'UTR
c.1512+58G>A
Unknown
0
Details
ACVRL1
Intron 01
c.1-34C>T
None
5.3
35
Details
ACVRL1
Intron 01
c.1-38C>T
None
14
24, 65, 77
Details
ACVRL1
Exon 03
c.207C>T
p.Cys69Cys
0
Details
ACVRL1
Intron 03
c.313+11C>T
None
40
27, 65
Details
ACVRL1
Intron 03
c.313+40G>A
None
0
Details
ACVRL1
Intron 03
c.314-35A>G
None
55
73, 77
Details
ACVRL1
Intron 03
c.314-49G>C
None
0
Details
ACVRL1
Intron 03
c.314-49G>A
unknown
1.4
78
Details
ACVRL1
Exon 04
c.330G>A
p.Ser110Ser
1.8
77, 78
Details
ACVRL1
Exon 04
c.381G>A
p.Leu127Leu
0
Details
ACVRL1
Exon 04
c.474A>T
p.Gly158Gly
0
69
Details
ACVRL1
Intron 05
c.625+110del21
None
50
73
Details
ACVRL1
Intron 05
c.626-60_59delGGinsT
None
0
35, 65
Details
ACVRL1
Intron 05
c.626-59delG
unknown
1.4
78
Details
ACVRL1
Intron 05
c.626-53C>T
None
0
73
Details
ACVRL1
Exon 06
c.666C>T
p.His222His
0.7
73
Details
ACVRL1
Exon 06
c.747G>A
p.Val249Val
2
24, 65
Details
ACVRL1
Intron 06
c.773-59insT
unknown
2.8
78
Details
ACVRL1
Exon 07
c.931G>A
p.A311T
0
Details
ACVRL1
Exon 07
c.933G>A
p.Ala311Ala
0
65
Details
ACVRL1
Intron 07
c.1048+55_58delTCTC
unknown
0.7
78
Details
ACVRL1
Intron 07
c.1247-86_84ATA>TAT
0
Details
ACVRL1
Exon 08
c.1092C>T
p.Ile364Ile
0
65
Details
ACVRL1
Exon 08
c.1166G>A
C389Y
0
Details
ACVRL1
Intron 09
c.1377+45T>C
unknown
29.4
78
Details
ACVRL1
Intron 09
c.1377+65A>G
unknown
29.4
78
Details
ACVRL1
Intron 09
c.1378-62C>A
none
0
Details
ACVRL1
Intron 09
c.1378-30T>C
None
2
24
Details
ACVRL1
Exon 10
c.1445C>T
p.Ala482Val
0
33, 35, 47
Details
ACVRL1
Exon 10
c.1452G>A
p.Arg484Arg
0.7
73
Details