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HHT Mutation Database
Hereditary Hemorrhagic Telangiectasia
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Variants
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Gene Name
Location
DNA Change
Protein Change
Avg. Het. Frequency
Reference
Admin
ACVRL1
ENG
-
-
Showing 1 to 40 of 40.
ENG
Exon 01
c.14C>T
p.Thr5Met
2
3, 16, 48, 65
Details
ENG
Intron 01
c.67+14C>T
None
0
Details
ENG
Exon 02
c.120C>T
p.Gly40Gly
0.5
Details
ENG
Exon 02
c.207G>A
p.Leu69Leu
11
3, 16, 35, 65
Details
ENG
Intron 02
c.67+25G>T
None
0
16, 65
Details
ENG
Intron 02
c.219+25G>A
unkown
1.4
78
Details
ENG
Intron 02
c.219+22-23delCGinsG
...
Unknown
...
0.7
78
Details
ENG
Intron 02
c.219+25G>T
None
5
Details
ENG
Exon 03
c.225G>A
p.Pro75Pro
1.1
Details
ENG
Exon 03
c.234G>A
p.Leu78Leu
1.1
Details
ENG
Intron 03
c.360+91C>T
None
0
Details
ENG
Intron 03
c.360+21C>T
None
0
Details
ENG
Exon 04
c.388C>A
p.Pro130Ser
0
65
Details
ENG
Exon 05
c.572G>A
p.Gly191Asp
6.4
35, 48, 65
Details
ENG
Exon 05
c.590G>A
p.Arg197Gln
0.9
48
Details
ENG
Intron 05
c.689+66_67insC
None
0
Details
ENG
Intron 06
c.817-27delCT
unknown
0
78
Details
ENG
Intron 06
c.817-79C>A
None
0
Details
ENG
Intron 07
c.991+58A>T
None
0
Details
ENG
Intron 07
c.991+25_26insCCTCCC
None
42.1
35, 65
Details
ENG
Exon 08
c.1029C>T
p.Thr343Thr
5
3, 35, 65
Details
ENG
Exon 08
c.1055C>T
p.Pro352Leu
1
16
Details
ENG
Exon 08
c.1060C>T
p.Leu354Leu
1.6
Details
ENG
Exon 08
c.1095C>T
p.D365D
0
Details
ENG
Exon 08
c.1096G>C
p.Asp366His
1
16, 21, 35, 48, 55, 65
Details
ENG
Intron 08
c.1134+54C>T
unknown
0.7
78
Details
ENG
Intron 08
c.1134+93G>T
None
0
Details
ENG
Intron 09a
c.1273-4G>A
None
1.25
73
Details
ENG
Exon 10
c.1374A>G
p.Pro458Pro
2
69, 73
Details
ENG
Exon 10
c.1407G>A
p.Pro469Pro
0.7
78
Details
ENG
Exon 11
c.1671C>T
p.T557T
0
Details
ENG
Intron 11
c.686+99T>A
None
0
Details
ENG
Exon 12
c.1724T>C
p.Ile575Thr
0.7
16, 65
Details
ENG
Intron 12
c.1741G>A
None
0
Details
ENG
Intron 12
c.1741+35G>A
None
0
Details
ENG
Intron 12
c.1742-72T>C
None
3.6
Details
ENG
Intron 12
c.1742-31T>C
unknown
0.7
78
Details
ENG
Exon 13
c.1794T>C
p.Gly598Gly
0
Details
ENG
Exon 13
c.1794T>G
p.Gly598Gly
1.2
48
Details
ENG
Exon 14
c.1932C>T
p.Ile644Ile
1.4
78
Details