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HHT Mutation Database
Hereditary Hemorrhagic Telangiectasia
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Variants
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Gene Name
Location
DNA Change
Protein Change
Reference
Admin
ACVRL1
ENG
-
Showing 1 to 28 of 28.
ENG
5'UTR
c.1-9G>A
78
Details
ENG
Exon 01
c.35T>C
p.Lys12Pro
Details
ENG
Exon 01
c.35T>G
p.Leu12Arg
Details
ENG
Exon 01
c.67delA
p.Ser23fs
Details
ENG
Intron 01
c.68-18C>A
Unknown
69
Details
ENG
Exon 02
c.95T>A
p.Leu32His
78
Details
ENG
Exon 02
c.179_180CC>AA
p.Ala60Glu
Details
ENG
Intron 02
c.219+22C>T
Unknown
69
Details
ENG
Exon 03
c.290T>G
p.Leu97Arg
78
Details
ENG
Exon 03
c.360C>T
p.Tyr120Tyr
Details
ENG
Intron 03
c.360+5G>C
Unknown
78
Details
ENG
Intron 03
c.361-113_109delTTCT
Unknown
69
Details
ENG
Exon 04
c.446G>C
p.Try149Ser
78
Details
ENG
Exon 04
c.494C>G
p.Pro165Arg
78
Details
ENG
Exon 05
c.580_591delTCGAGTGG
...
p.194_197delLeuGluTr
...
78
Details
ENG
Exon 05
c.614G>C
p.Arg205Pro
78
Details
ENG
Exon 05
c.659T>A
p.Ile220Asp
78
Details
ENG
Exon 05
c.659_660delTCinsAT
p.Ile220Asp
78
Details
ENG
Exon 07
c.872_883del12
p.Lys291_Asp294del
78
Details
ENG
Exon 07
c.875T>A
p.L292H
Details
ENG
Exon 07
c.899T>C
p.Leu300Pro
78
Details
ENG
Exon 08
c.1076T>C
p.I359T
Details
ENG
Exon 08
c.1119_1121delGAA
p.K374del
Details
ENG
Exon 09a
c.1235G>A
p.Cys412Tyr
78
Details
ENG
Exon 11
c.1445C>T
p.Ala482Val
78
Details
ENG
Exon 11
c.1452C>T
p.S484S
Details
ENG
Exon 11
c.1595T>C
p.Phe532Ser
78
Details
ENG
Exon 11
c.1634G>A
p.Gly545Asp
81
Details